Doença de Erdheim-Chester: relato de caso / Erdheim-Chester disease: a case report Erdheim-Chester disease: a case report

Rafaela Veras de Almeida, Alan Rodrigues Cavalcante, Bruno Alberto Falcão Pereira, Ricardo Mendes Rogério, Amanda luiza Silva de Aguiar Ramos, Luciana Gabriela de Souza da Silva, Soane Cristina Silveira de Souza, Vivianne de Paula Reis Guimarães

Abstract


A  doença  de  Erdheim-Chester  é  uma  rara  histiocitose de células não-Langerhans, primeiramente descrita por  Jakob  Erdheim  e  William  Chester  em  1930  de  etiologia  desconhecida.  Clinicamente,  pode manifestar sinais e sintomas multiorgânico e  o  diagnóstico  baseia-se  em  achados  radiológicos  e  anatomopatológicos.  Foi  relatado  um  caso  da  doença  onde  se  estudaram os achados clínicos e radiológicos.


Keywords


Doença de Erdheim-Chester, Xantogranuloma, Imunohistoquímica.

References


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Erdheim-chester disease: a concise review

Erdheim-chester disease: consensus recommendations for evaluation, diagnosis, and treatment in the molecular era




DOI: https://doi.org/10.34119/bjhrv5n1-011

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